ye hai biochem...kamino acids...

Urea cycle:
bicarbonate->carboxyphosphate->carbamic acid->carbomoyl phosphate
carbomoyl phosphate synthetase
(ac block)

actual cycle:

carbomyl phos+ornithine->citrulline
ornithine transcarbomylase

citrulene+asparate->argininosuccinate - fumerate->arginine
argininosuccinate sythetase
argininosuccinase

arginine+urea->ornithine
arginase

argininosuccinate->fumarate

deficiencies:

brain swelling due to excess of glutamine

argininisuccinase def.
excess agrinine is supplied.per molecule of arginine,2 nitrogen excreted.


carbomoyl phosphate synthase def,or ornithine transcarbomoylase def.accumulates as glycine

and glutamine
benzoate and phenylacetate


Benzoyl CoA->hippurate
(all out,photo,paper,plug pt.)
phenylacetate->phenyl acetyl CoA->phenyl acetyl glutamine



uricotelic:purine uric acid.


entry points:
pyruvate:SAC GWOT(har jyot)
serine,ala,cysteine, glycine,typtophan,threonine

OAA:aspartate,asparagine
DN
DoN

alpha keto glutarate:herp(es) q
HERP Q
histadine,glutamine,glutamate,arginine,proline


Succinyl CoA
MoVIe
Mehtionine,valine,Isoluecine

alcaptonuria:homogentisate
all caps:homo(dostana) gents

maple syrup:KIVi
leucine,valine,Isoluecine

Phenylketonuria:phenylalanine hydroxylase

hydroxy laces?