Urea cycle:
bicarbonate->carboxyphosphate->carbamic acid->carbomoyl phosphate
carbomoyl phosphate synthetase
(ac block)
actual cycle:
carbomyl phos+ornithine->citrulline
ornithine transcarbomylase
citrulene+asparate->argininosuccinate - fumerate->arginine
argininosuccinate sythetase
argininosuccinase
arginine+urea->ornithine
arginase
argininosuccinate->fumarate
deficiencies:
brain swelling due to excess of glutamine
argininisuccinase def.
excess agrinine is supplied.per molecule of arginine,2 nitrogen excreted.
carbomoyl phosphate synthase def,or ornithine transcarbomoylase def.accumulates as glycine
and glutamine
benzoate and phenylacetate
Benzoyl CoA->hippurate
(all out,photo,paper,plug pt.)
phenylacetate->phenyl acetyl CoA->phenyl acetyl glutamine
uricotelic:purine uric acid.
entry points:
pyruvate:SAC GWOT(har jyot)
serine,ala,cysteine, glycine,typtophan,threonine
OAA:aspartate,asparagine
DN
DoN
alpha keto glutarate:herp(es) q
HERP Q
histadine,glutamine,glutamate,arginine,proline
Succinyl CoA
MoVIe
Mehtionine,valine,Isoluecine
alcaptonuria:homogentisate
all caps:homo(dostana) gents
maple syrup:KIVi
leucine,valine,Isoluecine
Phenylketonuria:phenylalanine hydroxylase
hydroxy laces?
Sunday, November 23, 2008
Subscribe to:
Post Comments (Atom)
No comments:
Post a Comment
Commentwa?